Dacryocystitis-osteopoikilosis syndrome
Dacryocystitis-osteopoikilosis syndrome
Definition
Dacryocystitis - osteopoikilosis is an exceedingly rare autosomal dominant disorder reported in only a few patients to date and is characterized by dacryocystitis due to lacrimal canal stenosis,and osteopoikilosis (demonastratedr adiologically as discrete spherical osteosclerotic lesions of 2-10mm in diameter).
Also known as Gunal-Seber-Basaran syndrome — per MONDO