Hereditary chronic pancreatitis
Hereditary chronic pancreatitis
Definition
Hereditary chronic pancreatitis (HCP), a rare inherited form of pancreatitis is defined as recurrent acute pancreatitis and/or chronic pancreatitis in two first-degree relatives or 3 or more second-degree relatives in 2 or more generations, for which no predisposing factors are identified. HCP is characterized by irreversible damage to both exocrine and endocrine components of the pancreas.
Also known as hereditary chronic pancreatitis, hereditary pancreatitis — per MONDO
Also identified as
- ICD9 577.8 per MONDO
- MESH C537262 per MONDO
- NCIT C95436 per MONDO
- OMIM 167800 per MONDO
- Orphanet 676 per MONDO
- SCTID 68072000 per MONDO
- UMLS C0238339 per MONDO
Affected Organs
| Organ | Involvement | Source |
|---|---|---|
| Alimentary part of gastrointestinal system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Alimentary part of gastrointestinal system | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Pancreas | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Pancreas | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |