Hailey-Hailey disease

Hailey-Hailey disease

Definition

Benign chronic familial pemphigus of Hailey-Hailey is characterized by rhagades mostly located in the armpits, inguinal and perineal folds (scrotum, vulva).

Also known as benign chronic familial pemphigus of Hailey-Hailey, benign chronic pemphigus, Hailey-Hailey disease, pemphigus, benign familial — per MONDO

Also identified as

Affected Organs

Organ Involvement Source
Integumental system Disease Has Associated Anatomic Site NCIT · CC BY 4.0
Skin of body Disease Has Primary Anatomic Site NCIT · CC BY 4.0