Familial pityriasis rubra pilaris
Familial pityriasis rubra pilaris
Definition
A rare chronic papulosquamous disorder of unknown etiology characterized by small follicular papules, scaly red-orange patches, and palmoplantar hyperkeratosis, which may progress to plaques or erythroderma. Although most of the cases are sporadic and acquired, a familial form of the disease exists.
Also known as Devergie's disease, hereditary pityriasis rubra pilaris, pityriasis rubra pilaris--familial type, PRP — per MONDO