Aplasia of lacrimal and salivary glands
Aplasia of lacrimal and salivary glands
Definition
Aplasia of the lacrimal and salivary glands (ALSG) is a rare autosomal dominant disorder characterized by aplasia, atresia or hypoplasia of the lacrimal and salivary glands leading to varying features since infancy such as recurrent eye infections, irritable eyes, epiphora, xerostomia, dental caries, dental erosion and oral inflammation.
Also known as ALSG, aplasia of lacrimal and salivary glands, congenital absence of lacrimal puncta and salivary glands — per MONDO