Arterial tortuosity syndrome
ICD-10 Code
Q87.82
Arterial tortuosity syndrome
Definition
Arterial tortuosity syndrome (ATS) is a rare connective tissue disorder characterized by tortuosity and elongation of the large and medium-sized arteries and a propensity towards aneurysm formation, vascular dissection, and stenosis of the pulmonary arteries.
Also known as arterial tortuosity syndrome — per MONDO