Central areolar choroidal dystrophy
ICD-10 Code
H31.22
Central areolar choroidal dystrophy
Definition
A hereditary macular disorder, usually presenting between the ages of 30-60, characterized by a large area of atrophy in the center of the macula and the loss or absence of photoreceptors, retinal pigment epithelium and choriocapillaris in this area, resulting in a progressive decrease in visual acuity.
Also known as areolar atrophy of the macula, CACD, central areolar choroidal sclerosis, choroidal dystrophy — per MONDO