Hypoplasminogenemia

Definition

A rare multi-system disease characterized by markedly impaired extracellular fibrinolysis leading to the formation of ligneous (fibrin-rich) pseudomembranes on mucosae.

Also known as hypoplasminogenemia, plasminogen deficiency type 1, plasminogen deficiency, type 1, plasminogen deficiency, type I, type 1 plasminogen deficiency — per MONDO

Also identified as

• DOID 0111592 per MONDO
• ICD9 372.39 per MONDO
• MESH C580017 per MONDO
• OMIM 217090 per MONDO
• Orphanet 722 per MONDO
• Orphanet 97231 per MONDO
• SCTID 403435005 per MONDO
• SCTID 95840007 per MONDO
• UMLS C1968804 per MONDO