Macular corneal dystrophy
ICD-10 Code
H18.55
Macular corneal dystrophy
Definition
Macular corneal dystrophy (MCD) is a rare, severe form of stromal corneal dystrophy characterized by bilateral ill-defined cloudy regions within a hazy stroma, and eventually severe visual impairment.
Also known as corneal dystrophy Groenouw type II, Fehr corneal dystrophy, macular corneal dystrophy, MCD — per MONDO
Also identified as
- DOID 2565 per MONDO
- ICD10CM H18.55 per MONDO
- ICD9 371.55 per MONDO
- MESH C537834 per MONDO
- NCIT C34793 per MONDO
- OMIM 217800 per MONDO
- Orphanet 98969 per MONDO
- SCTID 60258001 per MONDO
- UMLS C1636149 per MONDO
Affected Organs
| Organ | Involvement | Source |
|---|---|---|
| Camera-type eye | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Camera-type eye | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Cornea | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Cornea | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |