Temtamy syndrome

Temtamy syndrome

Definition

Temtamy syndrome is a very rare congenital genetic neurological disorder characterized by agenesis/hypoplasia of corpus callosum with developmental abnormalities, ocular disorders, and variable craniofacial and skeletal abnormalities.

Also known as craniofacial dysmorphism-coloboma-corpus callosum agenesis syndrome, temtamy syndrome, Temtamy-Shalash syndrome — per MONDO

Also identified as