Ebstein anomaly
ICD-10 Code
Q22.5
Ebstein anomaly
Definition
Ebstein's malformation is a rare congenital cardiac anomaly characterized by rotational displacement of the septal and inferior leaflets of the tricuspid valve such that they are hinged within the right ventricle, rather than as expected at the atrioventricular junction.
Also known as Ebstein anomaly, Ebstein anomaly (disease), Ebstein anomaly of the tricuspid valve, Ebstein's anomaly, Ebstein's anomaly (disorder) [ambiguous], Ebstein's anomaly of tricuspid valve — per MONDO