Endocardial fibroelastosis

ICD-10 Code I42.4

Endocardial fibroelastosis

Definition

Endomyocardial fibroelastosis is a cause of unexplained childhood cardiac insufficiency. It results from diffuse thickening of the endocardium leading to dilated myocardiopathy in the majority of cases and restrictive myocardiopathy in rare cases. It may occur as a primary disorder or may be secondary to another cardiac malformation, notably aortic stenosis or atresia.

Also known as Elastomyofibrosis, endocardial fibroelastosis — per MONDO

Also identified as

Affected Organs

Organ Involvement Source
Cardiovascular system Disease Has Associated Anatomic Site NCIT · CC BY 4.0
Cardiovascular system Disease Has Primary Anatomic Site NCIT · CC BY 4.0
Heart Disease Has Associated Anatomic Site NCIT · CC BY 4.0
Heart Disease Has Primary Anatomic Site NCIT · CC BY 4.0
Respiratory system Disease Has Associated Anatomic Site NCIT · CC BY 4.0