Epidermodysplasia verruciformis
Epidermodysplasia verruciformis
Definition
A rare inherited genodermatosis characterized by chronic infection with human papillomavirus (HPV) leading to polymorphous cutaneous lesions and high risk of developing non melanoma skin cancer.
Also known as epidermodysplasia verruciformis, Lewandowsky-Lutz dysplasia, Lewandowsky-Lutz syndrome, Lutz-Lewandowsky epidermodysplasia verruciformis — per MONDO
Also identified as
- DOID 13777 per MONDO
- ICD9 078.19 per MONDO
- ICD9 757.8 per MONDO
- MESH D004819 per MONDO
- NCIT C126877 per MONDO
- Orphanet 302 per MONDO
- SCTID 19138001 per MONDO
- UMLS C0014522 per MONDO
Affected Organs
| Organ | Involvement | Source |
|---|---|---|
| Integumental system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Skin of body | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |