Hepatic veno-occlusive disease-immunodeficiency syndrome
Hepatic veno-occlusive disease-immunodeficiency syndrome
Definition
Hepatic veno-occlusive disease-immunodeficiency syndrome is characterized by the association of severe hypogammaglobulinemia, combined T and B cell immunodeficiency, absent lymph node germinal centers, absent tissue plasma cells and hepatic veno-occlusive disease.
Also known as VODI syndrome — per MONDO