Dubin-Johnson syndrome
Dubin-Johnson syndrome
Definition
Dubin-Johnson syndrome (DJS) is a benign, inherited liver disorder characterized clinically by chronic, predominantly conjugated, hyperbilirubinemia and histopathologically by black-brown pigment deposition in parenchymal liver cells.
Also known as chronic idiopathic jaundice, Dubin Johnson Syndrome, Dubin-Johnson syndrome, Dubin-Sprinz disease, hyperbilirubinemia type 2, Sprinz-Nelson syndrome — per MONDO