Hyperlysinemia

Hyperlysinemia

Definition

Hyperlysinaemia is a lysine metabolism disorder characterized by elevated levels of lysine in the cerebrospinal fluid and blood. Variable degrees of saccharopinuria are also present.

Also known as hyperlysinemia, hyperlysinemia (disease), hyperlysinemia type I, lysine alpha-ketoglutarate reductase deficiency — per MONDO

Also identified as