Nemaline myopathy 2
Nemaline myopathy 2
Definition
An autosomal recessive inherited myopathy caused by mutations in the NEB gene. It is characterized by generalized hypotonia and skeletal muscle weakness.
Also known as NEB nemaline myopathy, NEM2, nemaline myopathy 2, nemaline myopathy caused by mutation in NEB, nemaline myopathy type 2 — per MONDO
Also identified as
- DOID 0110928 per MONDO
- MESH C538349 per MONDO
- NCIT C118784 per MONDO
- OMIM 256030 per MONDO
- UMLS C1850569 per MONDO
Affected Organs
| Organ | Involvement | Source |
|---|---|---|
| Musculature | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Musculature | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Musculoskeletal system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Musculoskeletal system | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |