Subacute sclerosing panencephalitis
ICD-10 Code
A81.1
Subacute sclerosing panencephalitis
Definition
A chronic progressive encephalitis that develops a few years after measles infection and presents with a demyelination of the cerebral cortex.
Also known as Immunosuppressive measles encephalitis, SSPE, Subacute inclusion body encephalitis, Subacute sclerosing panencephalitis, Subacute sclerosing panencephalitis (disorder) [ambiguous], Van Bogaert disease, Van Bogaert encephalitis — per MONDO
Also identified as
- DOID 8970 per MONDO
- ICD10CM A81.1 per MONDO
- ICD9 046.2 per MONDO
- MESH D013344 per MONDO
- NCIT C85171 per MONDO
- OMIM 260470 per MONDO
- Orphanet 2806 per MONDO
- UMLS C0038522 per MONDO
Affected Organs
| Organ | Involvement | Source |
|---|---|---|
| Brain | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Brain | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Central nervous system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Central nervous system | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Nervous system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Nervous system | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |