Hyperimmunoglobulinemia D with periodic fever
Hyperimmunoglobulinemia D with periodic fever
Definition
Hyperimmunoglobinemia D with periodic fever (HIDS) is a rare autoinflammatory disease characterized by periodic attacks of fever and a systemic inflammatory reaction (cervical lymphadenopathy, abdominal pain, vomiting, diarrhea, arthralgias and skin signs).
Also known as HIDS, hyper-IgD syndrome, hyperimmunoglobinemia D with recurrent fever, hyperimmunoglobulinemia D syndrome, partial mevalonate kinase deficiency — per MONDO