Desquamative interstitial pneumonia
ICD-10 Code
J84.117
Desquamative interstitial pneumonia
Definition
A rare idiopathic interstitial pneumonia characterized by accumulation of macrophages in alveolar spaces and interstitial inflammation. It usually occurs in smokers. Some patients develop progressive interstitial lung fibrosis.
Also known as desquamative interstitial pneumonia, RBILD, respiratory bronchiolitis interstitial lung disease — per MONDO
Also identified as
- DOID 0050158 per MONDO
- ICD10CM J84.117 per MONDO
- ICD9 516.34 per MONDO
- ICD9 516.37 per MONDO
- MESH C562470 per MONDO
- NCIT C35288 per MONDO
- OMIM 263000 per MONDO
- Orphanet 98852 per MONDO
- SCTID 8549006 per MONDO
- UMLS C0238378 per MONDO
Affected Organs
| Organ | Involvement | Source |
|---|---|---|
| Lungs | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Lungs | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Respiratory system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Respiratory system | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |