Congenital pulmonary lymphangiectasia
Congenital pulmonary lymphangiectasia
Definition
Congenital pulmonary lymphangiectasia (PL) is a rare developmental disorder involving the lung and characterized by pulmonary subpleural, interlobar, perivascular, and peribronchial lymphatic dilatation.
Also known as congenital pulmonary lymphangiectasis, Diffuse Pulmonary Lymphangiomatosis, pulmonary lymphangiomatosis — per MONDO
Also identified as
- MESH C537727 per MONDO
- NCIT C99034 per MONDO
- OMIM 265300 per MONDO
- Orphanet 2414 per MONDO
- SCTID 45142002 per MONDO
- UMLS C1849554 per MONDO
Affected Organs
| Organ | Involvement | Source |
|---|---|---|
| Cardiovascular system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Cardiovascular system | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Lungs | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Lungs | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Respiratory system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Respiratory system | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |