Alveolar capillary dysplasia with misalignment of pulmonary veins

Alveolar capillary dysplasia with misalignment of pulmonary veins

Definition

A rare and fatal developmental lung disease characterized by respiratory distress in neonates due to refractory hypoxemia and severe pulmonary arterial hypertension.

Also known as ACDMPV, alveolar capillary dysplasia, alveolar capillary dysplasia with misalignment of pulmonary veins, alveolar capillary dysplasia with misalignment of pulmonary vessels, congenital alveolar capillary dysplasia, foetal circulation — per MONDO

Also identified as

Affected Organs

Organ Involvement Source
Lungs Disease Has Associated Anatomic Site NCIT · CC BY 4.0
Lungs Disease Has Primary Anatomic Site NCIT · CC BY 4.0
Respiratory system Disease Has Associated Anatomic Site NCIT · CC BY 4.0
Respiratory system Disease Has Primary Anatomic Site NCIT · CC BY 4.0