Embryonal rhabdomyosarcoma
Embryonal rhabdomyosarcoma
Definition
A poorly circumscribed morphologic variant of rhabdomyosarcoma. It is characterized by the presence of primitive skeletal muscle differentiation in any stage of myogenesis.
Also known as embryonal rhabdomyosarcoma, embryonal rhabdomyosarcoma (disease), ERMS, rhabdomyosarcoma, embryonal, type 1, rhabdomyosarcoma, somatic — per MONDO
Also identified as
- DOID 3246 per MONDO
- ICD9 171.9 per MONDO
- NCIT C8971 per MONDO
- OMIM 268210 per MONDO
- Orphanet 99757 per MONDO
- SCTID 404051002 per MONDO
- UMLS C0206656 per MONDO
Affected Organs
| Organ | Involvement | Source |
|---|---|---|
| Muscle tissue | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Musculature | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Musculoskeletal system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Striated muscle tissue | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |