Alveolar rhabdomyosarcoma
Alveolar rhabdomyosarcoma
Definition
A rapidly growing malignant mesenchymal neoplasm. It is characterized by the presence of round cells with myoblastic differentiation and a fibrovascular stroma resembling an alveolar growth pattern. The tumor usually presents in the extremities.
Also known as alveolar rhabdomyosarcoma, alveolar rhabdomyosarcoma (disease), alveolar rhabdomyosarcoma (morphologic abnormality), ARMS, monomorphous round cell rhabdomyosarcoma, paediatric alveolar rhabdomyosarcoma, pediatric alveolar rhabdomyosarcoma, rhabdomyosarcoma 2, alveolar, somatic mutation, rhabdomyosarcoma type 2, rhabdomyosarcoma, alveolar, somatic mutation — per MONDO
Also identified as
- DOID 4051 per MONDO
- ICD9 171.9 per MONDO
- MESH D018232 per MONDO
- NCIT C3749 per MONDO
- OMIM 268220 per MONDO
- Orphanet 99756 per MONDO
- SCTID 404053004 per MONDO
- UMLS C0206655 per MONDO
Affected Organs
| Organ | Involvement | Source |
|---|---|---|
| Muscle tissue | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Musculature | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Musculoskeletal system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Striated muscle tissue | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |