Schinzel-Giedion syndrome

Schinzel-Giedion syndrome

Definition

Schinzel-Giedion syndrome (SGS) is an ectodermal dysplasia syndrome chiefly characterized by a distinctive facial dysmorphism, hydronephrosis, severe developmental delay, typical skeletal malformations, and genital and cardiac anomalies.

Also known as Schinzel Giedion Syndrome, Schinzel-Giedion midface-retraction syndrome, Schinzel-Giedion syndrome, SGS — per MONDO

Also identified as