Spondyloepimetaphyseal dysplasia with joint laxity, type 1, with or without fractures

Spondyloepimetaphyseal dysplasia with joint laxity, type 1, with or without fractures

Definition

Any spondyloepimetaphyseal dysplasia with joint laxity in which the cause of the disease is a mutation in the B3GALT6 gene.

Also known as B3GALT6 spondyloepimetaphyseal dysplasia with joint laxity, SEMDJL1, spondyloepimetaphyseal dysplasia with joint laxity caused by mutation in B3GALT6, spondyloepimetaphyseal dysplasia with joint laxity, Beighton type, spondyloepimetaphyseal dysplasia with joint laxity, type 1, with or without fractures — per MONDO

Also identified as