Wiskott-Aldrich syndrome
ICD-10 Code
D82.0
Wiskott-Aldrich syndrome
Definition
Wiskott-Aldrich syndrome (WAS) is a primary immunodeficiency disease characterized by microthrombocytopenia, eczema, infections and an increased risk for autoimmune manifestations and malignancies.
Also known as eczema-thrombocytopenia-immunodeficiency syndrome, immunodeficiency 2, WAS, Wiskott Aldrich syndrome, Wiskott-Aldrich syndrome, Wiskott-Aldrich syndrome 1, Wiskott-Aldrich syndrome, X-linked recessive — per MONDO