Bazex-Dupre-Christol syndrome
Bazex-Dupre-Christol syndrome
Definition
Bazex-Dupre-Christol syndrome is a rare genodermatosis (hereditary skin disease) with a predisposition to early-onset basal cell carcinomas.
Also known as acrokeratosis of Bazex, acrokeratosis paraneoplastica, acrokeratosis paraneoplastica of Bazex, Bazex syndrome, Bazex syndrome, X-linked dominant, Bazex-Dupre-Christol syndrome, BDCS, follicular atrophoderma and basal cell carcinomas — per MONDO