Duchenne muscular dystrophy
Duchenne muscular dystrophy
Definition
Duchenne muscular dystrophy (DMD) is a neuromuscular disease characterized by rapidly progressive muscle weakness and wasting due to degeneration of skeletal, smooth and cardiac muscle.
Also known as DMD, Duchenne muscular dystrophy, Duchenne muscular dystrophy, X-linked recessive, severe dystrophinopathy, Duchenne type — per MONDO
Also identified as
- DOID 11723 per MONDO
- MESH D020388 per MONDO
- NCIT C75482 per MONDO
- OMIM 310200 per MONDO
- Orphanet 98896 per MONDO
- SCTID 76670001 per MONDO
- UMLS C0013264 per MONDO
Affected Organs
| Organ | Involvement | Source |
|---|---|---|
| Musculature | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Musculature | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Musculoskeletal system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Musculoskeletal system | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Nervous system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Nervous system | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Peripheral nervous system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Peripheral nervous system | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
Drugs indicated
| Drug | Relation | Source |
|---|---|---|
| Deflazacort | may treat | MEDRT · Public domain (U.S. Government work) |
| Givinostat | may treat | MEDRT · Public domain (U.S. Government work) |