Bladder exstrophy
Bladder exstrophy
Definition
Bladder exstrophy (or classic bladder exstrophy; CEB) is a congenital genitourinary malformation belonging to the spectrum of the exstrophy-epispadias complex (EEC) and is characterized by an evaginated bladder plate, epispadias and an anterior defect of the pelvis, pelvic floor and abdominal wall.
Also known as bladder exstrophy, bladder exstrophy (disease), classic exstrophy of the bladder, ectopia vesicae — per MONDO
Also identified as
- DOID 0080174 per MONDO
- ICD9 753.5 per MONDO
- MESH D001746 per MONDO
- NCIT C123207 per MONDO
- Orphanet 93930 per MONDO
- SCTID 61758007 per MONDO
- UMLS C0005689 per MONDO
Affected Organs
| Organ | Involvement | Source |
|---|---|---|
| Genitourinary system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Genitourinary system | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Renal system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Renal system | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Urinary bladder | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Urinary bladder | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |