Progressive bifocal chorioretinal atrophy
Progressive bifocal chorioretinal atrophy
Definition
Progressive bifocal chorioretinal atrophy (PBCRA) is an early-onset chorioretinal dystrophy characterized by large atrophic macular and nasal retinal lesions, nystagmus, myopia, poor vision, and slow disease progression.
Also known as CRAPB, PBCRA, progressive bifocal chorioretinal atrophy — per MONDO