Thiel-Behnke corneal dystrophy

Definition

Thiel-Behnke corneal dystrophy (TBCD) is a rare form of superficial corneal dystrophy characterized by sub-epithelial honeycomb-shaped corneal opacities in the superficial cornea, and progressive visual impairment.

Also known as anterior limiting membrane dystrophy type 2, anterior limiting membrane dystrophy type II, corneal dystrophy of Bowman layer type 2, corneal dystrophy of Bowman layer type II, curly fiber corneal dystrophy, curly fibre corneal dystrophy, honeycomb corneal dystrophy, TBCD, Thiel-Behnke corneal dystrophy, Waardenburg-Jonker corneal dystrophy — per MONDO

Also identified as

• DOID 0060455 per MONDO
• ICD9 371.52 per MONDO
• MESH C535942 per MONDO
• OMIM 602082 per MONDO
• Orphanet 98960 per MONDO
• SCTID 417065002 per MONDO
• UMLS C1562894 per MONDO