Malignant atrophic papulosis
Malignant atrophic papulosis
Definition
Malignant atrophic papulosis (MAP) is a rare, chronic, thrombo-obliterative vasculopathy characterized by papular skin lesions with central porcelain-white atrophy and a surrounding teleangiectatic rim. Systemic lesions may affect the gastrointestinal tract and the central nervous system (CNS) and are potentially lethal.
Also known as Degos Disease, Kohlmeier-Degos disease, Kohlmeier-Degos-Delort-Tricort syndrome, malignant atrophic papulosis, papulosis atrophican maligna — per MONDO