Dystrophic epidermolysis bullosa pruriginosa
Dystrophic epidermolysis bullosa pruriginosa
Definition
Dystrophic epidermolysis bullosa pruriginosa is a rare subtype of dystrophic epidermolysis bullosa (DEB) characterized by generalized or localized skin lesions associated with severe, if not intractable, pruritus.
Also known as DEB-Pr, DEB, pruriginosa, dystrophic epidermolysis bullosa pruriginosa, pruriginous dystrophic epidermolysis bullosa — per MONDO