Alpha thalassemia spectrum
ICD-10 Code
D56.0
Alpha thalassemia spectrum
Definition
An inherited hemoglobinopathy characterized by impaired synthesis of alpha-globin chains leading to a variable clinical picture depending on the number of affected alleles.
Also known as alpha thalassaemia, alpha thalassemia spectrum, alpha-thalassemia, thalassemia, alpha-, thalassemias, alpha- — per MONDO