CINCA syndrome

CINCA syndrome

Definition

Chronic Infantile Neurological, Cutaneous, and Articular (CINCA) syndrome is characterized by skin rash, joint involvement, chronic meningitis with granulocytes and, in some cases, sensorineural hearing loss and ocular signs.

Also known as chronic infantile neurological cutaneous and articular syndrome, chronic neurologic cutaneous and articular syndrome, CINCA syndrome, CINCA/NOMID, cryopyrin-associated periodic syndrome 3, infantile-onset multisystem inflammatory disease, IOMID syndrome, Neonatal-Onset Multisystem Inflammatory Disease, NOMID, NOMID syndrome, Prieur-Griscelli syndrome — per MONDO

Also identified as