Dermatofibrosarcoma protuberans
Dermatofibrosarcoma protuberans
Definition
Dermatofibrosarcoma protuberans (DFSP) is a rare infiltrating soft tissue sarcoma, generally of low grade malignancy, arising from the dermis of the skin and characteristically associated with a specific chromosomal translocation t(17;22).
Also known as dermatofibrosarcoma, dermatofibrosarcoma protuberans, DFSP — per MONDO
Also identified as
- DOID 3507 per MONDO
- MESH D018223 per MONDO
- NCIT C4683 per MONDO
- OMIM 607907 per MONDO
- Orphanet 31112 per MONDO
- SCTID 276799004 per MONDO
- UMLS C3693482 per MONDO
Affected Organs
| Organ | Involvement | Source |
|---|---|---|
| Dermis | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Integumental system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Skin of body | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Skin of body | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
Drugs indicated
| Drug | Relation | Source |
|---|---|---|
| Imatinib | may treat | MEDRT · Public domain (U.S. Government work) |