Capillary malformation-arteriovenous malformation syndrome
Capillary malformation-arteriovenous malformation syndrome
Definition
This syndrome is characterized by the association of multiple capillary malformations (CM) with an arteriovenous malformation (AVM) and arteriovenous fistulas.
Also known as CM-AVM — per MONDO
Also identified as
- ICD9 747.69 per MONDO
- MESH C564254 per MONDO
- NCIT C179668 per MONDO
- Orphanet 137667 per MONDO
- SCTID 703533007 per MONDO
- UMLS C1842180 per MONDO
Affected Organs
| Organ | Involvement | Source |
|---|---|---|
| Capillaries | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Cardiovascular system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Cardiovascular system | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |