Granulomatosis with polyangiitis
ICD-10 Code
M31.3
Granulomatosis with polyangiitis
Definition
A small-vessel necrotizing vasculitis characterized by the association of inflammation of the vessel wall and peri- and extravascular granulomatosis.
Also known as GPA, granulomatosis - Wegener's, granulomatosis with polyangiitis, necrotizing respiratory granulomatosis, pauci-immune glomerulonephritis associated with granulomatosis with polyangiitis, Wegener granulomatosis, Wegener's granulomatosis, Wegener's syndrome — per MONDO
Also identified as
- DOID 12132 per MONDO
- ICD10CM M31.3 per MONDO
- ICD9 446.4 per MONDO
- MESH D014890 per MONDO
- NCIT C123111 per MONDO
- NCIT C3444 per MONDO
- OMIM 608710 per MONDO
- Orphanet 900 per MONDO
- SCTID 195353004 per MONDO
- UMLS C3495801 per MONDO
Affected Organs
| Organ | Involvement | Source |
|---|---|---|
| Adult mammalian kidney | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Adult mammalian kidney | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Artery | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Cardiovascular system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Cardiovascular system | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Genitourinary system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Genitourinary system | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Renal system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Renal system | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
Drugs indicated
| Drug | Relation | Source |
|---|---|---|
| Cyclophosphamide | may treat | MEDRT · Public domain (U.S. Government work) |
| Rituximab | may treat | MEDRT · Public domain (U.S. Government work) |