Posterior column ataxia-retinitis pigmentosa syndrome

Posterior column ataxia-retinitis pigmentosa syndrome

Definition

Posterior column ataxia - retinitis pigmentosa is characterized by the association of progressive sensory ataxia and retinitis pigmentosa.

Also known as ataxia, posterior column, with retinitis pigmentosa, autosomal recessive posterior column ataxia and retinitis pigmentosa, PCARP — per MONDO

Also identified as