Permanent neonatal diabetes mellitus-pancreatic and cerebellar agenesis syndrome

Permanent neonatal diabetes mellitus-pancreatic and cerebellar agenesis syndrome

Definition

Permanent neonatal diabetes mellitus-pancreatic and cerebellar agenesis syndrome is characterized by neonatal diabetes mellitus associated with cerebellar and/or pancreatic agenesis.

Also known as pancreatic and cerebellar agenesis — per MONDO

Also identified as