Multiple endocrine neoplasia type 4

Multiple endocrine neoplasia type 4

Definition

Multiple endocrine neoplasia type 4 (MEN4) is a very rare form of MEN, an inherited cancer syndrome, characterized by parathyroid and anterior pituitary tumors, possibly associated with adrenal, renal, and reproductive organ tumors.

Also known as CDKN1B multiple endocrine neoplasia, MEN4, multiple endocrine neoplasia caused by mutation in CDKN1B, multiple endocrine neoplasia type 4, multiple endocrine neoplasia, type IV — per MONDO

Also identified as

Affected Organs

Organ Involvement Source
Endocrine gland Disease Has Associated Anatomic Site NCIT · CC BY 4.0
Endocrine gland Disease Has Primary Anatomic Site NCIT · CC BY 4.0