Autoimmune pulmonary alveolar proteinosis

Definition

Pulmonary alveolar proteinosis (PAP) is a rare lung disease characterized by the accumulation of a lipoproteinaceous substance in the distal air spaces which positively stains with periodic acid-Schiff (PAS).

Also known as APAP, autoimmune PAP, idiopathic PAP, idiopathic pulmonary alveolar proteinosis, iPAP — per MONDO

Also identified as

• MESH C567049 per MONDO
• OMIM 610910 per MONDO
• Orphanet 747 per MONDO
• SCTID 707443007 per MONDO
• UMLS C1970472 per MONDO