Kawasaki disease
ICD-10 Code
M30.3
Kawasaki disease
Definition
A rare inflammatory disease characterized by an acute febrile, systemic, self-limiting, medium-vessel vasculitis primarily affecting children. It often causes acute coronary arteritis which is associated with coronary arterial aneurysms (CAA) that may be life threatening when untreated.
Also known as acute febrile mucocutaneous lymph node syndrome, acute febrile mucocutaneous lymph node syndrome [MCLS], infantile polyarteritis nodosa, Kawasaki syndrome, mucocutaneous lymph node syndrome — per MONDO
Also identified as
- DOID 13378 per MONDO
- ICD10CM M30.3 per MONDO
- ICD9 446.1 per MONDO
- MESH D009080 per MONDO
- NCIT C34825 per MONDO
- OMIM 611775 per MONDO
- Orphanet 2331 per MONDO
- SCTID 75053002 per MONDO
- UMLS C0026691 per MONDO
Affected Organs
| Organ | Involvement | Source |
|---|---|---|
| Cardiovascular system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |