Proximal 16p11.2 microdeletion syndrome

Proximal 16p11.2 microdeletion syndrome

Definition

A chromosomal anomaly characterized by developmental and language delays, mild intellectual disability, social impairments (autism spectrum disorders), mild variable dysmorphism and predisposition to obesity.

Also known as autism susceptibility 14A, chromosome 16p11.2 deletion syndrome, 593kb, proximal del(16)(p11.2), proximal monosomy 16p11.2 — per MONDO

Also identified as