Dystonia 16
Dystonia 16
Definition
Dystonia 16 (DYT16) is a very rare and newly discovered movement disorder which is characterized by early-onset progressive limb dystonia, laryngeal and oromandibular dystonia, and parkinsonism.
Also known as dystonia 16, dystonia type 16, dystonic disorder caused by mutation in PRKRA, DYT-PRKRA, DYT16, early-onset dystonia parkinsonism, PRKRA dystonic disorder — per MONDO
Also identified as
- DOID 0090048 per MONDO
- MESH C567430 per MONDO
- NCIT C168729 per MONDO
- OMIM 612067 per MONDO
- Orphanet 210571 per MONDO
- SCTID 722435003 per MONDO
- UMLS C2677567 per MONDO
Affected Organs
| Organ | Involvement | Source |
|---|---|---|
| Central nervous system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Central nervous system | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Nervous system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Nervous system | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |