Congenital plasminogen activator inhibitor type 1 deficiency
Congenital plasminogen activator inhibitor type 1 deficiency
Definition
Congenital plasminogen activator inhibitor type 1 (PAI-1) deficiency is a rare genetic bleeding disorder characterized by premature lysis of hemostatic clots and a moderate bleeding tendency.
Also known as congenital PAI-1 deficiency, congenital plasminogen activator inhibitor type 1 deficiency — per MONDO