Primary sclerosing cholangitis

ICD-10 Code K83.01

Primary sclerosing cholangitis

Definition

Primary sclerosing cholangitis (PSC) is a rare, slowly progressive liver disease characterized by inflammation and destruction of the intra- and/or extra-hepatic bile ducts that lead to cholestasis, liver fibrosis, liver cirrhosis and ultimately liver failure.

Also known as PSC — per MONDO

Also identified as

Affected Organs

Organ Involvement Source
Alimentary part of gastrointestinal system Disease Has Associated Anatomic Site NCIT · CC BY 4.0
Alimentary part of gastrointestinal system Disease Has Primary Anatomic Site NCIT · CC BY 4.0
Bile ducts Disease Has Associated Anatomic Site NCIT · CC BY 4.0
Bile ducts Disease Has Primary Anatomic Site NCIT · CC BY 4.0
Biliary system Disease Has Associated Anatomic Site NCIT · CC BY 4.0