Pulmonary alveolar proteinosis
Pulmonary alveolar proteinosis
Definition
A rare lung disorder characterized by the filling of the pulmonary alveoli with proteinaceous material which stains positive with periodic acid-Schiff stain. It may be idiopathic or secondary due to hematologic malignancies or the inhalation of mineral dusts. Signs and symptoms include dyspnea, cough and low grade fever.
Also known as pulmonary alveolar proteinosis — per MONDO
Also identified as
- DOID 12120 per MONDO
- ICD9 516.0 per MONDO
- MESH D011649 per MONDO
- NCIT C85037 per MONDO
- SCTID 10501004 per MONDO
- UMLS C5400698 per MONDO
Affected Organs
| Organ | Involvement | Source |
|---|---|---|
| Lungs | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Lungs | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Respiratory system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Respiratory system | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |