Cryopyrin-associated periodic syndrome
Cryopyrin-associated periodic syndrome
Definition
Cryopyrin associated periodic syndrome (CAPS) defines a group of autoinflammatory diseases, characterized by recurrent episodes of systemic inflammatory attacks in the absence of infection or autoimmune disease. CAPS comprises 3 disorders on a continuum of severity: severe CINCA syndrome, intermediate Muckle-Wells syndrome (MWS) and milder familial cold urticaria (FCAS).
Also known as Cryopyrinopathy — per MONDO
Also identified as
- ICD9 759.89 per MONDO
- MESH D056587 per MONDO
- NCIT C84657 per MONDO
- Orphanet 208650 per MONDO
- SCTID 430079001 per MONDO
- UMLS C2316212 per MONDO
Drugs indicated
| Drug | Relation | Source |
|---|---|---|
| Anakinra | may treat | MEDRT · Public domain (U.S. Government work) |
| Canakinumab | may treat | MEDRT · Public domain (U.S. Government work) |